GTX130920
CLN5 antibody
Eine Lieferung in diese Region ist nicht möglich.
- SKU:
- GTX130920
- Zusätzliche Namen:
- CLN5 intracellular trafficking protein
- Anwendung:
- WB
- Konzentration:
- 1.13 mg/ml
- Physischer Zustand:
- Liquid
- Spezies-Reaktivität:
- Human
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Hersteller:
- Genetex
- Host:
- Rabbit
- Reaktivitäten:
- Human
- Buffer:
- PBS, 20% Glycerol, 0.025% ProClin 300.
- Immunogen:
- Recombinant protein encompassing a sequence within the center region of human CLN5. The exact sequence is proprietary.
- Uniprot:
- O75503
- Synonyme:
- ceroid-lipofuscinosis neuronal protein 5;ceroid-lipofuscinosis, neuronal 5
- Weitere Details:
- This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.
- Versandbedingungen:
- Blue Ice