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  2. Polyclonal

GTX114502

IVD antibody

Eine Lieferung in diese Region ist nicht möglich.

SKU:
GTX114502
Zusätzliche Namen:
isovaleryl-CoA dehydrogenase , ACAD2
Anwendung:
WB, IHC-P, IF, ICC
Konzentration:
1 mg/ml
Physischer Zustand:
Liquid
Spezies-Reaktivität:
Human
Aufreinigung:
Affinity Purified
Lagerbedingungen:
-20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Hersteller:
Genetex
Host:
Rabbit
Reaktivitäten:
Human, Mouse, Rat
Buffer:
0.1M Tris, 0.1M Glycine, 20% Glycerol, 0.01% Thimerosal.
Immunogen:
Recombinant protein encompassing a sequence within the center region of human IVD. The exact sequence is proprietary.
Uniprot:
P26440
Synonyme:
ACAD2;butyryl-CoA dehydrogenase;epididymis secretory sperm binding protein;isovaleryl Coenzyme A dehydrogenase;isovaleryl-CoA dehydrogenase, mitochondrial;IVDH
Weitere Details:
Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. [provided by RefSeq]
Versandbedingungen:
Blue Ice