COG8 antibody [N3C3]

Eine Lieferung in diese Region ist nicht möglich.

SKU:: GTX110375
Zusätzliche Namen:: component of oligomeric golgi complex 8 , CDG2H , DOR1
Anwendung:: WB, IF, ICC
Konzentration:: 1 mg/ml
Physischer Zustand:: Liquid
Spezies-Reaktivität:: Human
Aufreinigung:: Affinity Purified
Lagerbedingungen:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Hersteller:: Genetex
Host:: Rabbit
Reaktivitäten:: Human
Buffer:: PBS, 1% BSA, 20% Glycerol, 0.01% Thimerosal.
Immunogen:: Recombinant protein encompassing a sequence within the center region of human COG8. The exact sequence is proprietary.
Klon:: N3C3
Uniprot:: Q96MW5
Synonyme:: CDG2H;COG complex subunit 8;Component of oligomeric Golgi complex 8;conserved oligomeric golgi complex component 8;conserved oligomeric Golgi complex subunit 8;dependent on RIC1;DOR1
Weitere Details:: This gene encodes a protein that is a component of the conserved oligomeric Golgi (COG) complex, a multiprotein complex that plays a structural role in the Golgi apparatus, and is involved in intracellular membrane trafficking and glycoprotein modification. Mutations in this gene cause congenital disorder of glycosylation, type IIh, a disease that is characterized by under-glycosylated serum proteins, and whose symptoms include severe psychomotor retardation, failure to thrive, seizures, and dairy and wheat product intolerance. [provided by RefSeq]

Versandbedingungen:: Blue Ice