GTX105504
NAGLU antibody
Eine Lieferung in diese Region ist nicht möglich.
- SKU:
- GTX105504
- Zusätzliche Namen:
- N-acetyl-alpha-glucosaminidase , CMT2V , MPS-IIIB , MPS3B , NAG , UFHSD
- Anwendung:
- IHC-P, IHC-Fr, IF, ICC
- Konzentration:
- 0.69 mg/ml
- Physischer Zustand:
- Liquid
- Spezies-Reaktivität:
- Human
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Hersteller:
- Genetex
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse, Rat
- Buffer:
- PBS, 20% Glycerol, 0.025% ProClin 300.
- Immunogen:
- Recombinant protein encompassing a sequence within the center region of human NAGLU. The exact sequence is proprietary.
- Uniprot:
- P54802
- Synonyme:
- alpha-N-acetylglucosaminidase;CMT2V;MPS-IIIB;MPS3B;N-acetyl-alpha-glucosaminidase;N-acetylglucosaminidase, alpha;NAG;testicular tissue protein Li 18;UFHSD
- Weitere Details:
- This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate. [provided by RefSeq]
- Versandbedingungen:
- Blue Ice