![SGSH antibody [C1C3]](https://www.genetex.com/upload/website/prouct_img/normal/GTX101700/GTX101700_IHC_w_23060100_810.webp)
![SGSH antibody [C1C3]](https://www.genetex.com/upload/website/prouct_img/normal/GTX101700/GTX101700_WB_w_23060100_981.webp)
GTX101700
SGSH antibody [C1C3]
Eine Lieferung in diese Region ist nicht möglich.
- SKU:
- GTX101700
- Zusätzliche Namen:
- N-sulfoglucosamine sulfohydrolase , HSS , MPS3A , SFMD
- Anwendung:
- WB, IHC-P
- Konzentration:
- 1 mg/ml
- Physischer Zustand:
- Liquid
- Spezies-Reaktivität:
- Human
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Hersteller:
- Genetex
- Host:
- Rabbit
- Reaktivitäten:
- Human
- Buffer:
- 0.1M Tris, 0.1M Glycine, 10% Glycerol, 0.01% Thimerosal.
- Immunogen:
- Recombinant protein encompassing a sequence within the C-terminus region of human SGSH. The exact sequence is proprietary.
- Klon:
- C1C3
- Uniprot:
- P51688
- Synonyme:
- heparan sulfate sulfatase;HSS;MPS3A;mucopolysaccharidosis type IIIA;N-sulphoglucosamine sulphohydrolase;SFMD;sulfoglucosamine sulfamidase;sulphamidase
- Weitere Details:
- This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined. [provided by RefSeq]
- Versandbedingungen:
- Blue Ice