Galactosidase alpha antibody [N1C2]

Eine Lieferung in diese Region ist nicht möglich.

SKU:: GTX101178
Zusätzliche Namen:: galactosidase alpha , GALA
Anwendung:: WB, IHC-P, IP
Konzentration:: 0.16 mg/ml
Physischer Zustand:: Liquid
Spezies-Reaktivität:: Human
Aufreinigung:: Affinity Purified
Lagerbedingungen:: -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Hersteller:: Genetex
Host:: Rabbit
Reaktivitäten:: Human, Rat
Buffer:: PBS, 20% Glycerol, 0.025% ProClin 300.
Immunogen:: Recombinant protein encompassing a sequence within the center region of human Galactosidase alpha. The exact sequence is proprietary.
Klon:: N1C2
Uniprot:: P06280
Synonyme:: agalsidase alfa;alpha-D-galactosidase A;Alpha-D-galactoside galactohydrolase;alpha-D-galactoside galactohydrolase 1;alpha-gal A;alpha-galactosidase A;GALA;galactosylgalactosylglucosylceramidase GLA;melibiase
Weitere Details:: This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties. [provided by RefSeq]

Versandbedingungen:: Blue Ice