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  1. Alles ansehen
  2. Polyclonal

GTX100032

ACADM antibody

Eine Lieferung in diese Region ist nicht möglich.

SKU:
GTX100032
Zusätzliche Namen:
acyl-CoA dehydrogenase medium chain , ACAD1 , MCAD , MCADH
Anwendung:
WB, IHC-P, IF, ICC
Konzentration:
1 mg/ml
Physischer Zustand:
Liquid
Spezies-Reaktivität:
Human
Aufreinigung:
Affinity Purified
Lagerbedingungen:
-20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
Hersteller:
Genetex
Host:
Rabbit
Reaktivitäten:
Human
Buffer:
PBS, 20% Glycerol, 0.01% Thimerosal.
Immunogen:
Carrier-protein conjugated synthetic peptide encompassing a sequence within the C-terminus region of human ACADM. The exact sequence is proprietary.
Uniprot:
P11310
Synonyme:
ACAD1;acyl-CoA dehydrogenase, C-4 to C-12 straight chain;acyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chain;MCAD;MCADH;medium-chain acyl-CoA dehydrogenase;medium-chain specific acyl-CoA dehydrogenase, mitochondrial;testicular tissue protein Li 7
Weitere Details:
This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq]
Versandbedingungen:
Blue Ice