GTX03465
CLN6 antibody
Eine Lieferung in diese Region ist nicht möglich.
- SKU:
- GTX03465
- Zusätzliche Namen:
- CLN6 transmembrane ER protein , CLN4A , HsT18960 , nclf
- Anwendung:
- WB, IHC-P
- Konzentration:
- 1 mg/ml
- Physischer Zustand:
- Liquid
- Spezies-Reaktivität:
- Human
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., 2-8[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted., -20[o]C/-70[o]C Aliquot. Avoid freeze/thaw cycles. Store undiluted.
- Hersteller:
- Genetex
- Host:
- Rabbit
- Reaktivitäten:
- Human, Rat
- Buffer:
- PBS, 50% Glycerol, 0.02% sodium azide.
- Immunogen:
- Synthetic peptide, corresponding to amino acids 229-274 of Human CLN6.
- Uniprot:
- Q9NWW5
- Synonyme:
- ceroid-lipofuscinosis neuronal 6 late infantile;ceroid-lipofuscinosis neuronal protein 6;ceroid-lipofuscinosis, neuronal 6, late infantile;CLN4A;HsT18960;nclf
- Weitere Details:
- This gene is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely encode proteins involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function. [provided by RefSeq, Oct 2008]
- Versandbedingungen:
- Blue Ice