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E-AB-62750

GALC Polyclonal Antibody

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£195.30

War £217.00

SKU:
E-AB-62750
Zusätzliche Namen:
GALC
Anwendung:
IHC, WB
Konzentration:
1 mg/ml
Aufreinigung:
Affinity Purified
Lagerbedingungen:
-20[o]C Avoid freeze/thaw cycles.
Hersteller:
Elabscience
Host:
Rabbit
Reaktivitäten:
Human, Mouse, Rat
Buffer:
Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
Immunogen:
Recombinant fusion protein of human GALC (NP_000144.2).
Uniprot:
P54803
Synonyme:
galactocerebrosidase;galactocerebroside beta-galactosidase;Galactosylceramidase;galactosylceramide beta-galactosidase;galactosylceraminidase;GALCERase;testis tissue sperm-binding protein Li 88E;testis tissue sperm-binding protein Li 89A
Weitere Details:
This gene encodes a lysosomal protein which hydrolyzes the galactose ester bonds of galactosylceramide, galactosylsphingosine, lactosylceramide, and monogalactosyldiglyceride. Mutations in this gene have been associated with Krabbe disease, also known as globoid cell leukodystrophy. Alternate transcriptional splice variants, encoding different isoforms, have been characterized.
Versandbedingungen:
Blue Ice