E-AB-53204
VMA21 Polyclonal Antibody
Größe
£106.20
War £118.00
- SKU:
- E-AB-53204
- Zusätzliche Namen:
- Vacuolar ATPase Assembly Factor,MEAX,Myopathy With Excessive Autophagy,Myopathy With Excessive Autophagy Protein,VMA21,VMA21 Vacuolar H+-ATPase,VMA21 Vacuolar H+-ATPase Homolog (S. Cerevisiae),Vacuolar ATPase Assembly Integral Membrane Protein VMA21,XMEA
- Anwendung:
- IHC, IF
- Konzentration:
- 2.6 mg/ml
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Synthetic peptide of human VMA21
- Uniprot:
- Q3ZAQ7
- Synonyme:
- MEAX;myopathy with excessive autophagy protein;vacuolar ATPase assembly integral membrane protein VMA21;VMA21 vacuolar H+-ATPase homolog;VMA21, vacuolar ATPase assembly factor;XMEA
- Weitere Details:
- This gene encodes a chaperone for assembly of lysosomal vacuolar ATPase. Required for the assembly of the V0 complex of the vacuolar ATPase (V-ATPase) in the endoplasmic reticulum. Associates with the V0 complex of the vacuolar ATPase (V-ATPase). MEAX is a childhood-onset disease characterized by progressive vacuolation and atrophy of skeletal muscle. It is inherited in recessive fashion, affecting boys and sparing carrier females. Onset is in childhood, and patients exhibit weakness of the proximal muscles of the lower extremities, progressing slowly to involve other skeletal muscle groups over time.
- Versandbedingungen:
- Blue Ice