E-AB-53138
IDS Polyclonal Antibody

Größe
£106.20
War £118.00
- SKU:
- E-AB-53138
- Zusätzliche Namen:
- AW214631,Alpha L iduronate sulfate sulfatase,Alpha-L-iduronate sulfate sulfatase,IDS,Ids,Iduronate 2 sulfatase,Iduronate 2 sulfatase 14 kDa chain,Iduronate 2 sulfatase 42 kDa chain,Iduronate 2-sulfatase 14 kDa chain,Iduronate sulfatase,Idursulfase,MPS2,RP
- Anwendung:
- IHC
- Konzentration:
- 1.2 mg/ml
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Fusion protein of human IDS
- Uniprot:
- P22304
- Synonyme:
- alpha-L-iduronate sulfate sulfatase;ID2S;iduronate 2-sulfatase;iduronate 2-sulfatase 14 kDa chain;iduronate 2-sulfatase 42 kDa chain;idursulfase;MPS2;SIDS
- Weitere Details:
- Iduronate 2-sulfatase (IDS) is required for the lysosomal degradation of heparan sulfate and dermatan sulfate. Mutations causing IDS deficiency in humans result in the lysosomal storage of these glycosaminoglycans and Hunter syndrome,an X chromosome-linked disease. An internal proteolytic cleavage occurs to produce the mature IDS present in human liver shown to contain a 42 kDa polypeptide N-terminal to a 14 kDa polypeptide.
- Versandbedingungen:
- Blue Ice