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E-AB-53138

IDS Polyclonal Antibody

Größe

£106.20

War £118.00

SKU:
E-AB-53138
Zusätzliche Namen:
AW214631,Alpha L iduronate sulfate sulfatase,Alpha-L-iduronate sulfate sulfatase,IDS,Ids,Iduronate 2 sulfatase,Iduronate 2 sulfatase 14 kDa chain,Iduronate 2 sulfatase 42 kDa chain,Iduronate 2-sulfatase 14 kDa chain,Iduronate sulfatase,Idursulfase,MPS2,RP
Anwendung:
IHC
Konzentration:
1.2 mg/ml
Aufreinigung:
Affinity Purified
Lagerbedingungen:
-20[o]C Avoid freeze/thaw cycles.
Hersteller:
Elabscience
Host:
Rabbit
Reaktivitäten:
Human, Mouse
Buffer:
Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
Immunogen:
Fusion protein of human IDS
Uniprot:
P22304
Synonyme:
alpha-L-iduronate sulfate sulfatase;ID2S;iduronate 2-sulfatase;iduronate 2-sulfatase 14 kDa chain;iduronate 2-sulfatase 42 kDa chain;idursulfase;MPS2;SIDS
Weitere Details:
Iduronate 2-sulfatase (IDS) is required for the lysosomal degradation of heparan sulfate and dermatan sulfate. Mutations causing IDS deficiency in humans result in the lysosomal storage of these glycosaminoglycans and Hunter syndrome,an X chromosome-linked disease. An internal proteolytic cleavage occurs to produce the mature IDS present in human liver shown to contain a 42 kDa polypeptide N-terminal to a 14 kDa polypeptide.
Versandbedingungen:
Blue Ice