E-AB-52010
IDUA Polyclonal Antibody
Größe
£106.20
War £118.00
- SKU:
- E-AB-52010
- Zusätzliche Namen:
- Alpha L iduronidase,IDA,Iduronidase alpha L,MPS1
- Anwendung:
- IHC
- Konzentration:
- 0.78 mg/ml
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Synthetic peptide of human IDUA
- Uniprot:
- P35475
- Synonyme:
- alpha-L-iduronidase;IDA;iduronidase alpha-L-;MPS1;MPSI;mucopolysaccharidosis type I
- Weitere Details:
- This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate.This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans.Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
- Versandbedingungen:
- Blue Ice