E-AB-19774
CPS1 Polyclonal Antibody
Größe
£106.20
War £118.00
- SKU:
- E-AB-19774
- Zusätzliche Namen:
- Carbamoyl phosphate synthase,Carbamoyl phosphate synthase [ammonia],Carbamoyl phosphate synthase [ammonia] mitochondrial,Carbamoyl phosphate synthetase 1,Carbamoyl phosphate synthetase 1 mitochondrial,Carbamoyl phosphate synthetase I,Carbamoyl-phosphate s
- Anwendung:
- IHC
- Konzentration:
- 0.9 mg/ml
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse, Rat
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Synthetic peptide of human CPS1
- Uniprot:
- P31327
- Synonyme:
- carbamoyl-phosphate synthase (ammonia);carbamoyl-phosphate synthase [ammonia], mitochondrial;carbamoyl-phosphate synthase 1, mitochondrial;Carbamoyl-phosphate synthetase I;carbamoylphosphate synthetase I;CPSASE1;GATD6;PHN
- Weitere Details:
- The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation.
- Versandbedingungen:
- Blue Ice