E-AB-19032
GATM Polyclonal Antibody
Größe
£106.20
War £118.00
- SKU:
- E-AB-19032
- Zusätzliche Namen:
- mitochondrial,AGAT,AT,GATM,Glycine amidinotransferase,L-arginine:glycine amidinotransferase,Transamidinase,mitochondrial
- Anwendung:
- IHC
- Konzentration:
- 1.26 mg/ml
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse, Rat
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Fusion protein of human GATM
- Uniprot:
- P50440
- Synonyme:
- AGAT;AT;CCDS3;FRTS1;glycine amidinotransferase (L-arginine:glycine amidinotransferase);glycine amidinotransferase, mitochondrial;L-arginine:glycine amidinotransferase;testicular secretory protein Li 19;transamidinase
- Weitere Details:
- This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by cognitive disability, language impairment, and behavioral disorders.
- Versandbedingungen:
- Blue Ice