E-AB-18521
ASS1 Polyclonal Antibody
Größe
£106.20
War £118.00
- SKU:
- E-AB-18521
- Zusätzliche Namen:
- ASS,ASSA,ASSY,Argininosuccinate synthase,Argininosuccinate synthase 1,Argininosuccinate synthetase 1,Ass-1,CTLN1,Citrulline aspartate ligase,Citrulline--aspartate ligase,ass1
- Anwendung:
- IHC, WB
- Konzentration:
- 0.5 mg/ml
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse, Rat
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Fusion protein of human ASS1
- Uniprot:
- P00966
- Synonyme:
- argininosuccinate synthase;argininosuccinate synthetase 1;ASS;Citrulline--aspartate ligase;citrulline-aspartate ligase;CTLN1;epididymis secretory sperm binding protein
- Weitere Details:
- ASS1 is a rate-limiting enzyme in the urea cycle. Citrullinemia type I is an autosomal recessive disorder that is caused by a deficiency of the urea cycle enzyme argininosuccinate synthetase (ASS1). Deficiency of ASS1 shows various clinical manifestations encompassing severely affected patients with fatal neonatal hyperammonemia as well as asymptomatic individuals with only a biochemical phenotype.
- Versandbedingungen:
- Blue Ice