E-AB-15274
OTC Polyclonal Antibody
Größe
£106.20
War £118.00
- SKU:
- E-AB-15274
- Zusätzliche Namen:
- EC 2.1.3.3,MGC129967,MGC129968,MGC138856,OCTD,OTC,OTCase,Ornithine carbamoyltransferase,Ornithine carbamoyltransferase mitochondrial,Ornithine transcarbamylase,Otc,mitochondrial
- Anwendung:
- IHC, WB
- Konzentration:
- 0.3 mg/ml
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse, Rat
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Immunogen:
- Recombinant protein of human OTC
- Uniprot:
- P00480
- Synonyme:
- OCTD;ornithine carbamoyltransferase, mitochondrial;Ornithine transcarbamylase;ornithine transcarbamylase, mitochondrial;OTCase;OTCD
- Weitere Details:
- This nuclear gene encodes a mitochondrial matrix enzyme.Missense, nonsense, and frameshift mutations in this enzyme lead to ornithine transcarbamylase deficiency, which causes hyperammonemia.Since the gene for this enzyme maps close to that for Duchenne muscular dystrophy, it may play a role in that disease also.
- Versandbedingungen:
- Blue Ice