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E-AB-10769

ALDH6A1 Polyclonal Antibody

Größe

£106.20

War £118.00

SKU:
E-AB-10769
Zusätzliche Namen:
1110038I05Rik,AI314632,ALDH6A1,Aldehyde dehydrogenase 6 family member A1,Aldehyde dehydrogenase family 6,Aldehyde dehydrogenase family 6 member A1,Malonate semialdehyde dehydrogenase,Malonate-semialdehyde dehydrogenase [acylating],Methylmalon,subfamily A1
Anwendung:
IHC, WB
Konzentration:
0.4 mg/ml
Aufreinigung:
Affinity Purified
Lagerbedingungen:
-20[o]C Avoid freeze/thaw cycles.
Hersteller:
Elabscience
Host:
Rabbit
Reaktivitäten:
Human, Mouse, Rat
Buffer:
Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
Immunogen:
Recombinant protein of human ALDH6A1
Uniprot:
Q02252
Synonyme:
Aldehyde dehydrogenase family 6 member A1;malonate-semialdehyde dehydrogenase (acetylating);methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial;mitochondrial acylating methylmalonate-semialdehyde dehydrogenase;MMSADHA;MMSDH;testicular tissue protein Li 122
Weitere Details:
This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids.
Versandbedingungen:
Blue Ice