AN300183P
Recombinant Glucosamine (N-acetyl)-6-Sulfatase/G6S Monoclonal Antibody
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£361.80
War £402.00
- SKU:
- AN300183P
- Zusätzliche Namen:
- GNS,G6S,Glucosamine-6-Sulfatase,N-Acetylglucosamine-6-Sulfatase
- Anwendung:
- WB
- Konzentration:
- 1 mg/ml
- Aufreinigung:
- Protein A Purified
- Lagerbedingungen:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human
- Buffer:
- PBS
- Immunogen:
- Recombinant Human GNS protein
- Klon:
- B101
- Uniprot:
- P15586
- Synonyme:
- G6S;glucosamine -6-sulfatase;Glucosamine-6-sulfatase;N-acetylglucosamine-6-sulfatase
- Weitere Details:
- The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
- Versandbedingungen:
- Blue Ice