AN300124P
Recombinant ETHE1/HSCO Monoclonal Antibody
Größe
£361.80
War £402.00
- SKU:
- AN300124P
- Zusätzliche Namen:
- ETHE,YF13H,ETHE1,HSCO,YF13H12,ETHE1 protein,ethylmalonic encephalopathy 1,Ethylmalonic encephalopathy protein 1,hepatoma subtracted clone one,Hepatoma subtracted clone one protein,mitochondrial,mitochondrial precursor,Protein ETHE1,Protein ETHE1 mitochondrial
- Anwendung:
- WB, IP
- Konzentration:
- 1 mg/ml
- Aufreinigung:
- Protein A Purified
- Lagerbedingungen:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Rabbit
- Reaktivitäten:
- Human
- Buffer:
- PBS
- Immunogen:
- Recombinant Human ETHE1 / HSCO Protein
- Klon:
- A1238
- Uniprot:
- O95571
- Synonyme:
- ethylmalonic encephalopathy 1;Ethylmalonic encephalopathy protein 1;hepatoma subtracted clone one protein;HSCO;persulfide dioxygenase ETHE1, mitochondrial;protein ETHE1, mitochondrial;sulfur dioxygenase ETHE1;YF13H12
- Weitere Details:
- This gene encodes a member of the metallo beta-lactamase family of iron-containing proteins involved in the mitochondrial sulfide oxidation pathway. The encoded protein catalyzes the oxidation of a persulfide substrate to sulfite. Certain mutations in this gene cause ethylmalonic encephalopathy, an infantile metabolic disorder affecting the brain, gastrointestinal tract and peripheral vessels. Alternative splicing results in multiple transcript variants encoding different isoforms.
- Versandbedingungen:
- Blue Ice