AN200143P
Isovaleryl-CoA dehydrogenase/IVD Monoclonal Antibody

Größe
£311.40
War £346.00
- SKU:
- AN200143P
- Zusätzliche Namen:
- ACAD,IVD,ACAD2,FLJ12715,FLJ34849,Isovaleryl CoA dehydrogenase,Isovaleryl Coenzyme A dehydrogenase,Isovaleryl-CoA dehydrogenase,mitochondrial
- Anwendung:
- Flow Cytometry, WB, IF, ICC, IP
- Konzentration:
- 1 mg/ml
- Aufreinigung:
- Protein A Purified
- Lagerbedingungen:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Host:
- Mouse
- Reaktivitäten:
- Human
- Buffer:
- PBS
- Immunogen:
- Recombinant Human Isovaleryl-CoA dehydrogenase / IVD protein
- Klon:
- A991
- Uniprot:
- P26440
- Synonyme:
- ACAD2;butyryl-CoA dehydrogenase;epididymis secretory sperm binding protein;isovaleryl Coenzyme A dehydrogenase;isovaleryl-CoA dehydrogenase, mitochondrial;IVDH
- Weitere Details:
- Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
- Versandbedingungen:
- Blue Ice