Skip to content

Datenblatt ansehen

open_in_new
  1. Alles ansehen
  2. Monoclonal

AN200143P

Isovaleryl-CoA dehydrogenase/IVD Monoclonal Antibody

Größe

£311.40

War £346.00

SKU:
AN200143P
Zusätzliche Namen:
ACAD,IVD,ACAD2,FLJ12715,FLJ34849,Isovaleryl CoA dehydrogenase,Isovaleryl Coenzyme A dehydrogenase,Isovaleryl-CoA dehydrogenase,mitochondrial
Anwendung:
Flow Cytometry, WB, IF, ICC, IP
Konzentration:
1 mg/ml
Aufreinigung:
Protein A Purified
Lagerbedingungen:
-20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
Hersteller:
Elabscience
Host:
Mouse
Reaktivitäten:
Human
Buffer:
PBS
Immunogen:
Recombinant Human Isovaleryl-CoA dehydrogenase / IVD protein
Klon:
A991
Uniprot:
P26440
Synonyme:
ACAD2;butyryl-CoA dehydrogenase;epididymis secretory sperm binding protein;isovaleryl Coenzyme A dehydrogenase;isovaleryl-CoA dehydrogenase, mitochondrial;IVDH
Weitere Details:
Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
Versandbedingungen:
Blue Ice