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AN200137P

PHYH Monoclonal Antibody

Größe

£311.40

War £346.00

SKU:
AN200137P
Zusätzliche Namen:
LNAP,PHYH,LN1,LNAP1,PAHX,PHYH1,RD
Anwendung:
IHC-P
Konzentration:
1 mg/ml
Aufreinigung:
Protein A Purified
Lagerbedingungen:
-20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
Hersteller:
Elabscience
Host:
Mouse
Reaktivitäten:
Human
Buffer:
PBS
Immunogen:
Recombinant Human PHYH Protein
Klon:
A985
Uniprot:
O14832
Synonyme:
LN1;LNAP1;PAHX;PHYH1;phytanic acid oxidase;phytanoil-CoA alpha hydroxylase;phytanoyl-CoA 2 oxoglutarate dioxygenase;phytanoyl-CoA alpha-hydroxylase;phytanoyl-CoA dioxygenase, peroxisomal;RD
Weitere Details:
This gene is a member of the PhyH family and encodes a peroxisomal protein that is involved in the alpha-oxidation of 3-methyl branched fatty acids. Specifically, this protein converts phytanoyl-CoA to 1-hydroxyphytanoyl-CoA. Mutations in this gene have been associated with Refsum disease (RD) and deficient protein activity has been associated with Zellweger syndrome and rhizomelic chondrodysplasia punctata. Alternate transcriptional splice variants, encoding different isoforms, have been characterized.
Versandbedingungen:
Blue Ice