BCS1L Rabbit polyclonal antibody

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£152.00

SKU:: A7647
Zusätzliche Namen:: BCS|BCS1|BCS1L|BJS|FLNMS|GRACILE|h-BCS|h-BCS1|Hs.6719|MC3DN1|PTD
Anwendung:: ELISA, WB, IHC-P, IF, ICC
Molekulargewicht:: 48kDa
Spezies-Reaktivität:: Human
Aufreinigung:: Affinity Purified
Lagerbedingungen:: -20[o]C Avoid freeze/thaw cycles.
Hersteller:: Abclonal
Host:: Rabbit
Reaktivitäten:: Human, Mouse, Rat
Immunogen:: Recombinant protein (or fragment).This information is considered to be commercially sensitive.
Formulierung:: Unmodified
Sequenz:: RKGVQLGLVAFRRHYMITLEVPARDRSYAWLLSWLTRHSTRTQHLSVETSYLQHESGRISTKFEFVPSPGNHFIWYRGKWIRVERSREMQMIDLQTGTPWESVTFTALGTDRKVFFNILEEARELALQQEEGKTVMYTAVGSEWRPFGYPRRRRPLNSVVLQQGLADRIVRDVQEFIDNPKWYTDRGIPYRRGYLLYGPPGCGKSSFI
Uniprot:: Q9Y276
Synonyme:: BC1 (ubiquinol-cytochrome c reductase) synthesis-like;BCS;BCS1;BCS1-like protein;BJS;FLNMS;GRACILE;h-BCS;h-BCS1;Hs.6719;MC3DN1;mitochondrial chaperone BCS1;mitochondrial complex III assembly;PTD
Weitere Details:: This gene encodes a homolog of the S. cerevisiae bcs1 protein which is involved in the assembly of complex III of the mitochondrial respiratory chain. The encoded protein does not contain a mitochondrial targeting sequence but experimental studies confirm that it is imported into mitochondria. Mutations in this gene are associated with mitochondrial complex III deficiency and the GRACILE syndrome. Several alternatively spliced transcripts encoding two different isoforms have been described.