A4567
ACADM Rabbit monoclonal antibody

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- SKU:
- A4567
- Zusätzliche Namen:
- ACAD1|ACADM|MCAD|MCADH
- Anwendung:
- ELISA, WB, IHC-P, IF, ICC
- Molekulargewicht:
- 47kda
- Spezies-Reaktivität:
- Human
- Aufreinigung:
- Affinity Purified
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Abclonal
- Host:
- Rabbit
- Reaktivitäten:
- Human, Mouse, Rat
- Immunogen:
- Synthetic peptide. This information is considered to be commercially sensitive.
- Formulierung:
- Unmodified
- Sequenz:
- WYFLLARSDPDPKAPANKAFTGFIVEADTPGIQIGRKELNMGQRCSDTRGIVFEDVKVPKENVLIGDGAGFKVAMGAFDKTRPVVAAGAVGLAQRALDEAT
- Uniprot:
- P11310
- Synonyme:
- ACAD1;acyl-CoA dehydrogenase, C-4 to C-12 straight chain;acyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chain;MCAD;MCADH;medium-chain acyl-CoA dehydrogenase;medium-chain specific acyl-CoA dehydrogenase, mitochondrial;testicular tissue protein Li 7
- Weitere Details:
- This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
- Versandbedingungen:
- Blue Ice







