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A27999

HIBCH Rabbit monoclonal antibody

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SKU:
A27999
Zusätzliche Namen:
HIBYLCOAH
Anwendung:
ELISA, WB, IHC-P
Molekulargewicht:
40kda
Spezies-Reaktivität:
Human
Aufreinigung:
Affinity Purified
Lagerbedingungen:
-20[o]C Avoid freeze/thaw cycles.
Hersteller:
Abclonal
Host:
Rabbit
Reaktivitäten:
Human, Mouse, Rat
Immunogen:
Recombinant protein (or fragment).This information is considered to be commercially sensitive.
Formulierung:
Unmodified
Sequenz:
DAAEEVLLEKKGCTGVITLNRPKFLNALTLNMIRQIYPQLKKWEQDPETFLIIIKGAGGKAFCAGGDIRVISEAEKAKQKIAPVFFREEYMLNNAVGSCQKPYVALIHGITMGGGVGLSVHGQFRVATEKCLFAMPETAIGLFPDVGGGYFLPRLQGKLGYFLALTGFRLKGRDVYRAGIATHFVDSEKLAMLEEDLLALKSPSKENIASVLENYHTESKIDRDKSFILEEHMDKINSCFSANTVEEIIENLQQDGSSFALEQLKVINKMSPTSLKITLRQLMEGSSKTLQEVLTMEY
Uniprot:
Q6NVY1
Synonyme:
3-hydroxyisobutyryl-CoA hydrolase, mitochondrial;3-hydroxyisobutyryl-Coenzyme A hydrolase;HIB-CoA hydrolase;HIBYL-CoA-H;HIBYLCOAH;testicular tissue protein Li 86
Weitere Details:
This gene encodes the enzyme responsible for hydrolysis of both HIBYL-CoA and beta-hydroxypropionyl-CoA. Mutations in this gene have been associated with 3-hyroxyisobutyryl-CoA hydrolase deficiency. Alternative splicing results in multiple transcript variants.
Versandbedingungen:
Blue Ice