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A15181

MCCC2 Rabbit polyclonal antibody

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£152.00

SKU:
A15181
Zusätzliche Namen:
MCCB|MCCC2|MCCCbeta
Anwendung:
ELISA, WB, IHC-P, IF, ICC
Molekulargewicht:
61kDa
Spezies-Reaktivität:
Human
Aufreinigung:
Affinity Purified
Lagerbedingungen:
-20[o]C Avoid freeze/thaw cycles.
Hersteller:
Abclonal
Host:
Rabbit
Reaktivitäten:
Human, Mouse, Rat
Immunogen:
Recombinant protein (or fragment).This information is considered to be commercially sensitive.
Formulierung:
Unmodified
Sequenz:
LHLTRKVVRNLNYQKKLDVTIEPSEEPLFPADELYGIVGANLKRSFDVREVIARIVDGSRFTEFKAFYGDTLVTGFARIFGYPVGIVGNNGVLFSESAKKGTHFVQLCCQRNIPLLFLQNITGFMVGREYEAEGIAKDGAKMVAAVACAQVPKITLIIGGSYGAGNYGMCGRAYSPRFLYIWPNARISVMGGEQAANVLATITKDQRAREGKQFSSADEAALKEPIIKKFEEEGNPYYSSARVWDDGIIDPADTRLVLGLSFSAALNAPIEKTDFGIFRM
Uniprot:
Q9HCC0
Synonyme:
3-methylcrotonyl-CoA carboxylase 2;3-methylcrotonyl-CoA carboxylase non-biotin-containing subunit;3-methylcrotonyl-CoA:carbon dioxide ligase subunit beta;biotin carboxylase;MCCase subunit beta;MCCB;MCCCbeta;methylcrotonoyl-CoA carboxylase 2 (beta);methylcrotonoyl-CoA carboxylase beta chain, mitochondrial;methylcrotonoyl-Coenzyme A carboxylase 2 (beta);non-biotin containing subunit of 3-methylcrotonyl-CoA carboxylase;testicular secretory protein Li 29
Weitere Details:
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
Versandbedingungen:
Blue Ice