DMD rabbit pAb
Produktgrößen
50UL
£ POA
ES9017-50UL
100UL
£ POA
ES9017-100UL
Über dieses Produkt
- SKU:
- ES9017
- Anwendung:
- Immunohistochemistry, Immunofluorescence
- Klonalität:
- Polyclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- dystrophin(DMD) Homo sapiens The dystrophin gene is the largest gene found in nature; measuring 2.4 Mb. The gene was identified through a positional cloning approach; targeted at the isolation of the gene responsible for Duchenne (DMD) and Becker (BMD) Muscular Dystrophies. DMD is a recessive; fatal; X-linked disorder occurring at a frequency of about 1 in 3;500 new-born males. BMD is a milder allelic form. In general; DMD patients carry mutations which cause premature translation termination (nonsense or frame shift mutations); while in BMD patients dystrophin is reduced either in molecular weight (derived from in-frame deletions) or in expression level. The dystrophin gene is highly complex; containing at least eight independent; tissue-specific promoters and two polyA-addition sites. Furthermore; dystrophin RNA is differentially spliced; producing a range of different transcripts; encoding a large set of protein isoforms. Dystrophin (as enc
- Immunogen:
- Synthesized peptide derived from part region of human protein
- Isotyp:
- IgG
- Reaktivitäten:
- Human, Mouse, Rat
- Versandbedingungen:
- Blue Ice
- Quelle:
- Rabbit
- Lagerbedingungen:
- -20[o]C
- Hersteller:
- ELK Biotechnology
- Typ:
- Antibodies: Polyclonal Antibody