HEXA rabbit pAb
Produktgrößen
50UL
£ POA
ES3963-50UL
100UL
£ POA
ES3963-100UL
Über dieses Produkt
- SKU:
- ES3963
- Zusätzliche Namen:
- HEXA; Beta-hexosaminidase subunit alpha; Beta-N-acetylhexosaminidase subunit alpha; Hexosaminidase subunit A; N-acetyl-beta-glucosaminidase subunit alpha
- Anwendung:
- Western Blot, Immunohistochemistry, Immunofluorescence, ELISA
- Klonalität:
- Polyclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- This gene encodes a member of the glycosyl hydrolase 20 family of proteins. The encoded preproprotein is proteolytically processed to generate the alpha subunit of the lysosomal enzyme beta-hexosaminidase. This enzyme; together with the cofactor GM2 activator protein; catalyzes the degradation of the ganglioside GM2; and other molecules containing terminal N-acetyl hexosamines. Mutations in this gene lead to an accumulation of GM2 ganglioside in neurons; the underlying cause of neurodegenerative disorders termed the GM2 gangliosidoses; including Tay-Sachs disease (GM2-gangliosidosis type I). Alternative splicing results in multiple transcript variants; at least one of which encodes a preproprotein that is proteolytically processed. [provided by RefSeq; Jan 2016];
- Immunogen:
- Synthesized peptide derived from HEXA . at AA range: 121-170
- Isotyp:
- IgG
- Reaktivitäten:
- Human, Mouse, Rat
- Versandbedingungen:
- Blue Ice
- Quelle:
- Rabbit
- Lagerbedingungen:
- -20[o]C
- Hersteller:
- ELK Biotechnology
- Typ:
- Antibodies: Polyclonal Antibody
