FH Polyclonal Antibody
Produktgrößen
60 ul
£217,00
E-AB-61065-60UL
120 ul
£317,00
E-AB-61065-120UL
200 ul
£492,00
E-AB-61065-200UL
Über dieses Produkt
- SKU:
- E-AB-61065
- Zusätzliche Namen:
- FH,FMRD,HLRCC,LRCC,MCL,MCUL1
- Anwendung:
- Immunofluorescence, Western Blot
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Klonalität:
- Polyclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- The protein encoded by this gene is an enzymatic component of the tricarboxylic acid (TCA) cycle, or Krebs cycle, and catalyzes the formation of L-malate from fumarate. It exists in both a cytosolic form and an N-terminal extended form, differing only in the translation start site used. The N-terminal extended form is targeted to the mitochondrion, where the removal of the extension generates the same form as in the cytoplasm. It is similar to some thermostable class II fumarases and functions as a homotetramer. Mutations in this gene can cause fumarase deficiency and lead to progressive encephalopathy.
- Host:
- Rabbit
- Immunogen:
- Recombinant fusion protein of human FH (NP_000134.2).
- Isotyp:
- IgG
- Aufreinigung:
- Affinity Purified
- Reaktivitäten:
- Human, Mouse, Rat
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Typ:
- Antibody: Polyclonal Antibody
- Datenblatt des Herstellers:p-fh_polyclonal_antibody-e_ab_61065