TIMM8A Polyclonal Antibody
Produktgrößen
20 ul
£118,00
E-AB-52670-20UL
60 ul
£183,00
E-AB-52670-60UL
120 ul
£272,00
E-AB-52670-120UL
200 ul
£420,00
E-AB-52670-200UL
Über dieses Produkt
- SKU:
- E-AB-52670
- Zusätzliche Namen:
- DDP,DDP 1,DDP1,DFN 1,DFN1,Deafness dystonia protein 1,Deafness/dystonia peptide,MGC12262,MTS,Mitochondrial import inner membrane translocase subunit Tim8 A,TIM 8A,TIM8,TIM8A,TIMM 8A,Translocase of inner mitochondrial membrane 8 homolog A,X li,timm8a
- Anwendung:
- Immunohistochemistry
- Buffer:
- Phosphate buffered solution, pH 7.4, containing 0.05% stabilizer and 50% glycerol.
- Klonalität:
- Polyclonal
- Konzentration:
- 1.62 mg/ml
- Weitere Details:
- This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome, an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
- Host:
- Rabbit
- Immunogen:
- Fusion protein of human TIMM8A
- Isotyp:
- IgG
- Aufreinigung:
- Affinity Purified
- Reaktivitäten:
- Human, Mouse, Rat
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Typ:
- Antibody: Polyclonal Antibody
- Datenblatt des Herstellers:p-timm8a_polyclonal_antibody-e_ab_52670