Recombinant SPR Monoclonal Antibody
Produktgrößen
50 ul
£281,00
AN302028L-50UL
100 ul
£402,00
AN302028L-100UL
Über dieses Produkt
- SKU:
- AN302028L
- Zusätzliche Namen:
- SDR38C,member,OTTHUMP,SPR,SDR38C1,8 dihydrobiopterin:NADP+ oxidoreductase),member 1,OTTHUMP00000160199,Sepiapterin reductase,Sepiapterin reductase (7,Short chain dehydrogenase/reductase family 38C,SPRE
- Anwendung:
- Immunohistochemistry, Western Blot
- Buffer:
- PBS, 50% glycerol, 0.05% Proclin 300, 0.05% protein protectant.
- translate.label.attr.clone:
- A748
- Klonalität:
- Recombinant Monoclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- SPR can catalyze the final one or two reductions in tetra-hydrobiopterin biosynthesis to form 5,6,7,8-tetrahydrobiopterin.Defects in SPR are the cause of dystonia DOPA-responsive due to sepiapterin reductase deficiency (DRDSPRD). In the majority of cases, patients manifest progressive psychomotor retardation, dystonia and spasticity. Cognitive anomalies are also often present. The disease is due to severe dopamine and serotonin deficiencies in the central nervous system caused by a defect in BH4 synthesis.
- Host:
- Rabbit
- Immunogen:
- Peptide. This information is proprietary to PTMab.
- Isotyp:
- IgG, kappa
- Aufreinigung:
- Protein A Purified
- Reaktivitäten:
- Human
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Typ:
- Antibody: Recombinant Antibodies
- Datenblatt des Herstellers:p-recombinant_spr_monoclonal_antibody-an302028l