Recombinant alpha-Galactosidase A/GLA Monoclonal Antibody
Produktgrößen
20 ul
£189,00
AN300412P-20UL
100 ul
£402,00
AN300412P-100UL
Über dieses Produkt
- SKU:
- AN300412P
- Zusätzliche Namen:
- GLA,GALA,Alpha-D-Galactoside,Galactohydrolase,galactosidase alpha,GLAL,Melibiase,Agalsidase,Alpha-galactosidase A,Alpha-D-galactosidase A,Alpha-D-galactoside galactohydrolase,Galactosylgalactosylglucosylceramidase GLA
- Anwendung:
- Western Blot
- Buffer:
- PBS
- translate.label.attr.clone:
- B338
- Klonalität:
- Monoclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- alpha -Galactosidase A is a homodimeric glycoprotein that can release terminal alpha -galactosyl moieties from glycolipids and glycoproteins and catalyze the hydrolysis of melibiose into galactose and glucose . It is a lysosomal enzyme and is responsible for degradation of glycolipid globotriaosylceramide (Gb3) (Gal alpha 1-4Gal beta 1-4Glc beta -ceramide). Mutations in this gene cause Fabry disease, an X-linked hereditary lysosomal storage disease with the accumulation of Gb3 in the walls of small blood vessels, nerves, dorsal root ganglia, renal glomerular and tubular epithelial cells, and cardiomyocytes .
- Host:
- Rabbit
- Immunogen:
- Recombinant Human alpha-Galactosidase A/GLA protein
- Isotyp:
- IgG
- Aufreinigung:
- Protein A Purified
- Reaktivitäten:
- Human
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Typ:
- Antibody: Monoclonal Antibody
- Datenblatt des Herstellers:gla_monoclonal_antibody-an300412p