Recombinant Glucosamine (N-acetyl)-6-Sulfatase/G6S Monoclonal Antibody
Produktgrößen
100 ul
£402,00
AN300183P-100UL
Über dieses Produkt
- SKU:
- AN300183P
- Zusätzliche Namen:
- GNS,G6S,Glucosamine-6-Sulfatase,N-Acetylglucosamine-6-Sulfatase
- Anwendung:
- Western Blot
- Buffer:
- PBS
- translate.label.attr.clone:
- B101
- Klonalität:
- Recombinant Monoclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
- Host:
- Rabbit
- Immunogen:
- Recombinant Human GNS protein
- Isotyp:
- IgG
- Aufreinigung:
- Protein A Purified
- Reaktivitäten:
- Human
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles., 2-8[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Typ:
- Antibody: Recombinant Antibodies
- Datenblatt des Herstellers:g6s_monoclonal_antibody-an300183p