GLA Alpha/Galactosidase Alpha Polyclonal Antibody
Produktgrößen
25 ul
£134,00
AN006790L-25UL
100 ul
£291,00
AN006790L-100UL
Über dieses Produkt
- SKU:
- AN006790L
- Zusätzliche Namen:
- GLA;GALA;Alpha-D-Galactoside;Galactohydrolase;galactosidase alpha;GLAL;Melibiase;Agalsidase;Alpha-galactosidase A;Alpha-D-galactosidase A;Alpha-D-galactoside galactohydrolase;Galactosylgalactosylglucosylceramidase GLA
- Anwendung:
- Immunohistochemistry, Western Blot
- Buffer:
- PBS with 0.05% proclin 300, 1% protective protein and 50% glycerol,pH7.4
- Klonalität:
- Polyclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- alpha -Galactosidase A is a homodimeric glycoprotein that can release terminal alpha -galactosyl moieties from glycolipids and glycoproteins and catalyze the hydrolysis of melibiose into galactose and glucose . It is a lysosomal enzyme and is responsible for degradation of glycolipid globotriaosylceramide (Gb3) (Gal alpha 1-4Gal beta 1-4Glc beta -ceramide). Mutations in this gene cause Fabry disease, an X-linked hereditary lysosomal storage disease with the accumulation of Gb3 in the walls of small blood vessels, nerves, dorsal root ganglia, renal glomerular and tubular epithelial cells, and cardiomyocytes.
- Host:
- Rabbit
- Immunogen:
- Recombinant Human GLA Alpha/Galactosidase Alpha protein expressed by Mammalian
- Isotyp:
- IgG
- Aufreinigung:
- Affinity Purified
- Reaktivitäten:
- Human
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- -20[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Elabscience
- Typ:
- Antibody: Polyclonal Antibody
- Datenblatt des Herstellers:galactosidase_alpha_polyclonal_antibody-an006790l