DMD Antibody
Produktgrößen
50 ul
£186,00
CSB-PA503789-50UL
100 ul
£334,00
CSB-PA503789-100UL
Über dieses Produkt
- SKU:
- CSB-PA503789
- Zusätzliche Namen:
- BMD antibody; CMD3B antibody; DMD antibody; DMD_HUMAN antibody; Duchenne muscular dystrophy protein antibody; Dystrophin antibody; Muscular dystrophy Duchenne and Becker types antibody
- Anwendung:
- ELISA, Immunohistochemistry
- Buffer:
- PBS
- Klonalität:
- Polyclonal
- Weitere Details:
- The dystrophin gene is the largest gene found in nature, measuring 2.4 Mb. The gene was identified through a positional cloning approach, targeted at the isolation of the gene responsible for Duchenne (DMD) and Becker (BMD) Muscular Dystrophies. DMD is a recessive, fatal, X-linked disorder occurring at a frequency of about 1 in 3,500 new-born males. BMD is a milder allelic form. In general, DMD patients carry mutations which cause premature translation termination (nonsense or frame shift mutations), while in BMD patients dystrophin is reduced either in molecular weight (derived from in-frame deletions) or in expression level.
- Host:
- Rabbit
- Immunogen:
- Fusion protein of Human DMD
- Isotyp:
- IgG
- Physischer Zustand:
- Liquid
- Aufreinigung:
- Affinity Purified
- Reaktivitäten:
- Human, Mouse
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- -20[o]C/-70[o]C Avoid freeze/thaw cycles.
- Hersteller:
- Cusabio
- Typ:
- Antibody: Polyclonal Antibody
- Datenblatt des Herstellers:DMD-Antibody-11101262.html
