FH Antibody
Produktgrößen
100ul
£392,00
OASG02713-100UL
Über dieses Produkt
- SKU:
- OASG02713
- Zusätzliche Namen:
- MCL; FMRD; HsFH; LRCC; HLRCC; MCUL1
- Klonalität:
- Monoclonal
- Konzentration:
- 1 mg/ml
- Weitere Details:
- The protein encoded by this gene is an enzymatic component of the tricarboxylic acid (TCA) cycle; or Krebs cycle; and catalyzes the formation of L-malate from fumarate. It exists in both a cytosolic form and an N-terminal extended form; differing only in the translation start site used. The N-terminal extended form is targeted to the mitochondrion; where the removal of the extension generates the same form as in the cytoplasm. It is similar to some thermostable class II fumarases and functions as a homotetramer. Mutations in this gene can cause fumarase deficiency and lead to progressive encephalopathy.
- Gendetails:
- fumarate hydratase
- Host:
- Mouse
- Immunogen:
- Recombinant Protein
- Aufreinigung:
- The antibody was affinity-purified from mouse ascites by affinity-chromatography using specific immunogen.
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- Store at -20C. Avoid repeated freeze/thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Monoclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php