ETFA Antibody
Produktgrößen
100ul
£630,00
OAGA04639-100UL
Über dieses Produkt
- SKU:
- OAGA04639
- Zusätzliche Namen:
- EMA; GA2; MADD
- Klonalität:
- Polyclonal
- Konzentration:
- 0.91 mg/ml
- Weitere Details:
- ETFA participates in catalyzing the initial step of the mitochondrial fatty acid beta-oxidation. It shuttles electrons between primary flavoprotein dehydrogenases and the membrane-bound electron transfer flavoprotein ubiquinone oxidoreductase. Defects in electron-transfer-flavoprotein have been implicated in type II glutaricaciduria in which multiple acyl-CoA dehydrogenase deficiencies result in large excretion of glutaric; lactic; ethylmalonic; butyric; isobutyric; 2-methyl-butyric; and isovaleric acids. Two transcript variants encoding different isoforms have been found for this gene.
- Gendetails:
- electron transfer flavoprotein alpha subunit
- Host:
- Rabbit
- Immunogen:
- Recombinant protein encompassing a sequence within the center region of human ETFA. The exact sequence is proprietary.
- Isotyp:
- IgG
- Proteindetails:
- electron transfer flavoprotein subunit alpha; mitochondrial
- Aufreinigung:
- Purified by antigen-affinity chromatography.
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- Keep as concentrated solution. Aliquot and store at -20C or below. Avoid multiple freeze-thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php