GALNS Antibody
Produktgrößen
100 uL
£446,00
OAAJ07817-100UL
Über dieses Produkt
- SKU:
- OAAJ07817
- Zusätzliche Namen:
- GAS; MPS4A; GalN6S; GALNAC6S
- Klonalität:
- Polyclonal
- Konzentration:
- 1 mg/mL
- Weitere Details:
- This gene encodes N-acetylgalactosamine-6-sulfatase which is a lysosomal exohydrolase required for the degradation of the glycosaminoglycans; keratan sulfate; and chondroitin 6-sulfate. Sequence alterations including point; missense and nonsense mutations; as well as those that affect splicing; result in a deficiency of this enzyme. Deficiencies of this enzyme lead to Morquio A syndrome; a lysosomal storage disorder.
- Host:
- Rabbit
- Immunogen:
- Recombinant protein of human GALNS
- Molekulargewicht:
- 58 kDa
- Proteindetails:
- N-acetylgalactosamine-6-sulfatase
- Aufreinigung:
- Immunogen affinity chromatography
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- Store at +4C. For long term storage; aliquot and store at -20C. Avoid freeze/thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php