Anti-FKRP Polyclonal Antibody
Produktgrößen
100ug
£597,00
OAAI00760-100UG
Über dieses Produkt
- SKU:
- OAAI00760
- Zusätzliche Namen:
- FKTR;fukutin-related protein;LGMD2I;LGMDR9;MDC1C;MDDGA5;MDDGB5;MDDGC5;ribitol-5-phosphate transferase.
- Klonalität:
- Polyclonal
- Konzentration:
- 100ug/200ul
- Weitere Details:
- Fukutin-related protein (FKRP) is targeted to the medial Golgi appaRatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy; mental retardation; and cerebellar cysts. Mutations in fukutin-related protein (FKRP) give rise to mild and more severe forms of muscular dystrophy.
FKRP may influence the glycosylation status of dystroglycan from within the sarcolemmal dystrophin-glycoprotein complex.
FKRP associates with the sarcolemmal DGC and that it plays a unique role in dystroglycanopathy muscle disease. - Gendetails:
- fukutin related protein
- Host:
- Rabbit
- Immunogen:
- A synthetic peptide corresponding to the C-terminus of human FKRP protein. This sequence is identical to human; mouse and rat
- Isotyp:
- Rabbit IgG
- Aufreinigung:
- Affinity Purified
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- The antibodies are stable for 24 months from date of receipt when stored at -20C to -70C. The antibodies can be stored at 2C-8C for three month without detectable loss of activity. Avoid repeated freezing-thawing cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php