GCH1 antibody - C-terminal region
Produktgrößen
25ul
£177,00
ARP59618-P050-25UL
100 ul
£412,00
ARP59618-P050-100UL
Über dieses Produkt
- SKU:
- ARP59618-P050
- Zusätzliche Namen:
- GCH; DYT5; DYT14; DYT5a; GTPCH1; HPABH4B; GTP-CH-1
- Klonalität:
- Polyclonal
- Konzentration:
- 0.5 mg/ml
- Weitere Details:
- This gene encodes a member of the GTP cyclohydrolase family. The encoded protein is the first and rate-limiting enzyme in tetrahydrobiopterin (BH4) biosynthesis; catalyzing the conversion of GTP into 7;8-dihydroneopterin triphosphate. BH4 is an essential cofactor required by aromatic amino acid hydroxylases as well as nitric oxide synthases. Mutations in this gene are associated with malignant hyperphenylalaninemia and dopa-responsive dystonia. Several alternatively spliced transcript variants encoding different isoforms have been described; however; not all variants give rise to a functional enzyme.
- Gendetails:
- GTP cyclohydrolase 1
- Host:
- Rabbit
- Immunogen:
- The immunogen is a synthetic peptide directed towards the C terminal region of human GCH1
- Molekulargewicht:
- 28kDa
- Proteindetails:
- GTP cyclohydrolase 1
- Aufreinigung:
- Affinity Purified
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- For short term use; store at 2-8C up to 1 week. For long term storage; store at -20C in small aliquots to prevent freeze-thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php