GNS antibody - C-terminal region
Produktgrößen
25ul
£177,00
ARP45217-P050-25UL
100 ul
£412,00
ARP45217-P050-100UL
Über dieses Produkt
- SKU:
- ARP45217-P050
- Zusätzliche Namen:
- G6S
- Klonalität:
- Polyclonal
- Konzentration:
- 0.5 mg/ml
- Weitere Details:
- GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin; heparin sulphate; and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder ucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin; heparan sulphate; and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.
- Gendetails:
- Glucosamine (N-acetyl)-6-sulfatase
- Host:
- Rabbit
- Immunogen:
- The immunogen is a synthetic peptide directed towards the C terminal region of human GNS
- Molekulargewicht:
- 62kDa
- Proteindetails:
- N-acetylglucosamine-6-sulfatase
- Aufreinigung:
- Affinity Purified
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- For short term use; store at 2-8C up to 1 week. For long term storage; store at -20C in small aliquots to prevent freeze-thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php