FKTN Antibody - C-terminal region
Produktgrößen
25ul
£177,00
ARP45034-P050-25UL
100 ul
£412,00
ARP45034-P050-100UL
Über dieses Produkt
- SKU:
- ARP45034-P050
- Zusätzliche Namen:
- FCMD; CMD1X; LGMD2M; MDDGA4; MDDGB4; MDDGC4; LGMDR13
- Klonalität:
- Polyclonal
- Konzentration:
- 0.5 mg/ml
- Weitere Details:
- The protein encoded by this gene is a putative transmembrane protein that is localized to the cis-Golgi compartment; where it may be involved in the glycosylation of alpha-dystroglycan in skeletal muscle. The encoded protein is thought to be a glycosyltransferase and could play a role in brain development. Defects in this gene are a cause of Fukuyama-type congenital muscular dystrophy (FCMD); Walker-Warburg syndrome (WWS); limb-girdle muscular dystrophy type 2M (LGMD2M); and dilated cardiomyopathy type 1X (CMD1X). Alternatively spliced transcript variants have been found for this gene.
- Gendetails:
- fukutin
- Host:
- Rabbit
- Immunogen:
- The immunogen is a synthetic peptide directed towards the C-terminal region of human FKTN
- Molekulargewicht:
- 36kDa
- Proteindetails:
- fukutin
- Aufreinigung:
- Affinity Purified
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- For short term use; store at 2-8C up to 1 week. For long term storage; store at -20C in small aliquots to prevent freeze-thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php