GAA Antibody-N-terminal region
Produktgrößen
25ul
£177,00
ARP44227-P050-25UL
100 ul
£412,00
ARP44227-P050-100UL
Über dieses Produkt
- SKU:
- ARP44227-P050
- Zusätzliche Namen:
- LYAG
- Klonalität:
- Polyclonal
- Konzentration:
- 0.5 mg/ml
- Weitere Details:
- This gene encodes lysosomal alpha-glucosidase; which is essential for the degradation of glycogen to glucose in lysosomes. The encoded preproprotein is proteolytically processed to generate multiple intermediate forms and the mature form of the enzyme. Defects in this gene are the cause of glycogen storage disease II; also known as Pompe's disease; which is an autosomal recessive disorder with a broad clinical spectrum. Alternative splicing results in multiple transcript variants.
- Gendetails:
- glucosidase; alpha; acid
- Host:
- Rabbit
- Immunogen:
- The immunogen is a synthetic peptide directed towards the N terminal region of human GAA
- Molekulargewicht:
- 104 kDa
- Proteindetails:
- lysosomal alpha-glucosidase
- Aufreinigung:
- Affinity purified
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- For short term use; store at 2-8C up to 1 week. For long term storage; store at -20C in small aliquots to prevent freeze-thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php