GAA antibody - N-terminal region
Produktgrößen
25ul
£177,00
ARP44226-P050-25UL
100 ul
£412,00
ARP44226-P050-100UL
Über dieses Produkt
- SKU:
- ARP44226-P050
- Zusätzliche Namen:
- LYAG
- Klonalität:
- Polyclonal
- Konzentration:
- 0.5 mg/ml
- Weitere Details:
- GAA is acid alpha-glucosidase; which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II; also known as Pompe's disease; which is an autosomal recessive disorder with a broad clinical spectrum. This gene encodes acid alpha-glucosidase; which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II; also known as Pompe's disease; which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.
- Gendetails:
- Glucosidase; alpha; acid
- Host:
- Rabbit
- Immunogen:
- The immunogen is a synthetic peptide directed towards the N terminal region of human GAA
- Molekulargewicht:
- 98kDa
- Proteindetails:
- Lysosomal alpha-glucosidase
- Aufreinigung:
- Affinity Purified
- Versandbedingungen:
- Blue Ice
- Lagerbedingungen:
- For short term use; store at 2-8C up to 1 week. For long term storage; store at -20C in small aliquots to prevent freeze-thaw cycles.
- Hersteller:
- Aviva Systems Biology
- Typ:
- Antibodies: Polyclonal Antibody
- Datenblatt des Herstellers:html_datasheet.php